봉입소체근염의 증례를 통한 임상, 병리학적, 혈청학 고찰

A Case of Inclusion Body Myositis with Clinical, Pathological and Serological Consideration
  • 박영은; 
  • 강민성; 
  • 신진홍; 
  • 김대성

초록

Inclusion body myositis is a rare condition of idiopathic inflammatory myopathy. Prior criteria for the diagnosis of inclusion body myositis essentially required pathological features of rimmed vacuoles, tubulofilamentous inclusions, and amyloid deposits. However, recently developed new diagnostic criteria emphasize clinical characteristics including weakness of finger flexors and knee extensors. In addition, a serological evaluation of anti-cN1A antibody is helpful for the diagnosis. We report a case of inclusion body myositis with clinical, pathological, and serological consideration.

키워드

Inclusion body myositides; Pathology; Antibodies
제목
봉입소체근염의 증례를 통한 임상, 병리학적, 혈청학 고찰
제목 (타언어)
A Case of Inclusion Body Myositis with Clinical, Pathological and Serological Consideration
저자
박영은; 강민성; 신진홍; 김대성
발행일
2023-02
유형
Y
저널명
대한신경과학회지
권
41
호
1
페이지
31 ~ 34